가부키 증후군(Kabuki syndrome) 환자의 치과적 관리의 치험례
DENTAL MANAGEMENT OF A PATIENT WITH KABUKI SYNDROME : A CASE REPORT
강힘찬, 남옥형, 김미선, 최성철, 김광철, 이효설,
소속 상세정보
강힘찬 ( Kang Him-Chan ) - 경희대학교 치의학전문대학원 소아치과학교실
남옥형 ( Nam Ok-Hyung ) - 경희대학교 치의학전문대학원 소아치과학교실
김미선 ( Kim Mi-Sun ) - 강동경희대학교병원 치과병원 소아치과
최성철 ( Choi Sung-Chul ) - 경희대학교 치의학전문대학원 소아치과학교실
김광철 ( Kim Kwang-Chul ) - 강동경희대학교병원 치과병원 소아치과
이효설 ( Lee Hyo-Seol ) - 경희대학교 치의학전문대학원 소아치과학교실
Abstract
Kabuki syndrome is characterized by typical facial features (elongated palpebral fissures with eversion of the lateral third of the lower eyelid; arched and broad eyebrows; short columella with depressed nasal tip; large, prominent, or cupped ears), minor skeletal anomalies, persistence of fetal fingertip pads, mild to moderate intellectual disability, and postnatal growth deficiency.
A 6-year-old male with kabuki syndrome was referred from the local dental clinic for left facial swelling and dental caries on all primary molars. He was treated for acute periapical abscess with incision and drainage under physical restraint, and left maxillary second primary molar was extracted. Other caries treatment was performed under general anesthesia.
As the syndrome involves many different medical problems, special cares should be considered. Dental treatment should be carried out in comprehensive consultation system.
키워드
Kabuki syndrome; General anesthesia; Dental management
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